Yuav ua li cas yog Morgagni-Stewart-Morel syndrome?

Syndrome ntawm Morgagni-Stewart-Morel, yees duab qhia uas yuav tsum tau pom nyob rau hauv no tsab xov xwm, tsis tshua muaj - ib lab cov neeg muaj mob tag nrho tsuas yog ib puas thiab plaub caug. Ntxiv mus, nyob rau hauv kev xyaum, cov tub txawg fim mas nrog cov "thooj" ntawm tus kab mob, vim hais tias cov kab mob kev paub rau ntau xyoo, thiab cov tsos mob sib txawv speeds. Cov neeg mob yuav tsum tau soj ntsuam tsis yog ib tus kws kho mob ua ntej lub syndrome manifested siab thiab txiav txim seb lub caij nyoog mob.

Cov tseem ceeb heev lub xeev ntawm tus kab mob no nce mus txog, thaum nws cov ntaub ntawv ib tug pathological irreversible hloov nyob rau hauv lub cev. Tom qab ntawd, los pab tus neeg mob yog suab tsis yooj yim sua.

zaj dabneeg

Syndrome ntawm Morgagni-Stewart-Morel tau kom huv si piav nyob rau hauv 1762, thaum lub Italian pathologist Morgagni qhib neeg tuag tau plaub caug cov poj niam thiab pom thooj ntawm lub sab hauv ntawm lub frontal pob txha phaj. Nyob rau tib lub sij hawm, nws sau tseg rog thiab ntau lub cev plaub hau. Morgagni pom tej yam tshwm sim ntawm sib xyaw thiab piav nyob rau hauv kom meej nws pom. Tom qab ntawd, nyob rau thaum lawv tseem cov tsos mob pom Morel thiab Stewart tau ntxiv rau cov kev soj ntsuam daim duab ntawm ntau yam neurological thiab hlwb ces.

Yuav ua li cas yog kev mob nkees

Morgagni-Stewart-Morel syndrome - ib tug kab mob nyob rau hauv uas lub kuaj frontal hyperostosis puab pob txha phaj, rog thiab ib tug xov tooj ntawm lwm yam endocrine thiab metabolic mob. Mob nyob rau hauv lub loj heev feem ntau tshwm sim nyob rau hauv cov poj niam, mas tom qab plaub caug xyoo, tab sis tej zaum kuj tshwm sim thiab peb caug. Cov caug syndrome yuav luag tsis tshwm sim, nrog tsawg zam.

Etiology thiab pathogenesis

Kab Mob Morgagni-Stewart-Morel - syndrome, pathogenesis thiab etiology ntawm uas muaj ib tug hluas txhais. Ib co sau phau ntseeg hais tias tus pathology yog tshuaj ntsuam genetic thiab kis tau los ntawm autosomal hom hom. Muaj tswvyim hais tias cov syndrome yog zoo txuam nrog rau X-chromosome. Muaj ntau thaum tus kab mob no raug kev txom nyem plaub tiam, feem ntau cov poj niam.

Muaj cais tus neeg mob ntawm syndrome ces nyob rau hauv cov txiv neej. Tab sis lawv yog thawm, thiab cov science yog tseem tsis tau paub yuav ua li cas tus kab mob yog kis tau los ntawm cov txiv neej cov kab. Ib txhia ntseeg hais tias cov syndrome yog feem ntau pom nyob rau hauv cov poj niam thaum lub sij hawm lawm. Tab sis cov ntaub ntawv sau thaum lub sij hawm, muab tso rau hauv daim ntawv no mus rau hauv nqe lus nug.

Tus kab mob muaj peev xwm tshwm sim vim kab mob (tsuas yog sinusitis), neuroinfections thiab puas hlwb raug mob. Twb pom Morgagni-Stewart-Morel syndrome castrates cov poj niam uas tau muaj kev phais. Tej yam ntxwv ntawm lub syndrome tej zaum yuav tsim tom qab kev kho mob cancer.

Muaj ntau thaum tus kab mob no tau kuaj nyob rau hauv cov neeg mob uas:

• uterine myoma;
• sklerokistoz zes qe menyuam;
• pheej galactorrhea;
• qhov chaw mos infantilism.

Morgagni-Stewart-Morel syndrome: pathology

Thaum tus kab mob no tsis yog tsuas yog thicker puab frontal pob txha phaj, tab sis puav kuaj hyperostosis lub taub hau thiab fronto-occipital cheeb tsam. Muaj ntau ntau me me kev hloov nyob rau hauv lub endocrine qog. Ua lub xov tooj ntawm eosinophil thiab basophil hlwb. Pib adenomatous loj hlob (thyroid, adrenal cortex thiab t. D.).

cov tsos mob

Thaum ib tug neeg yog pom Morgagni-Stewart-Morel syndrome, muaj ib tug xov tooj ntawm cov tsos mob uas tuab nws:

• Cov neeg mob pib los ua kev mob taub hau.
• Rog, mas nyob rau hauv lub plab cheeb tsam.
• Daim tawv nqaij khaws ib tug li qub xim, tiam sis feem ntau tshwm sim pyoderma thiab quaj eczema.
• Nyob rau hauv feem ntau muaj yog ib tug qhia hypertrichosis.
• Nyob rau hauv daim tawv nqaij cim pastoznost pib swell lub sab nqua, zoo nkaus li akrozianoz.
• Nqaij tsis muaj zog.
• Muaj cov kev hloov nyob rau hauv cov hlab plawv system thiab ua pa kabmob (lub plawv expanding rau ib thaj tsam, muaj lag ntseg tones thiab lub plawv tsis ua hauj lwm).
• Lub nyiam cev qhuav dej, catarrh ntawm lub Upper pa ib ntsuj av tau thiab bronchopneumonia.
• Cov kev hloov nyob rau hauv lub endocrine qog cov yam ntxwv nta muaj. Txauv yuav ua tau li qub, ntau zog los yog poob.
• Tsis carbohydrate kam rau ua. Feem ntau cov ntshav qab zib yog kom meej meej manifested.

• Ntxhov cev ntas. Nyob rau hauv cev xeeb tub, thaum lub sij hawm lub sij hawm no tus neeg mob tus mob deteriorates.
• Muaj tshee thiab kev puas hlwb kev ntshawv siab. Lawv manifest lawv tus kheej nyob rau hauv daim ntawv ntawm cov kev xav lability, txob taus, insomnia thiab nyiam rau kev nyuaj siab.
• Internal frontal hyperostosis phaj yog feem ntau nyeem tas pob txha taub hau pob txha. Nyob rau hauv tej rooj plaub, txawm ua rau kom qhov luaj li cas ntawm cov Turkish eeb.

tus kab mob no

Morgagni-Stewart-Morel syndrome yuav ua rau lub cev nyob rau hauv ntau txoj kev. Feem ntau nws yog nyob ntawm cov neeg kawm ntawv ntawm cov rog. Qhia tau muaj ib tug zoo feem nyob rau hauv lub neej expectancy:

• kev ua si ntawm lub plawv yog ib qhov nyuaj;
• vim txuam nrog roj tshwm sim myocardium thiab cov pericardium;
• siab txoj hauj lwm ntawm lub diaphragm;
• ntshav, thiab nyob rau hauv ua ke nrog nrog atherosclerosis thiab tawg tsim lub plawv tsis ua hauj lwm, uas yog ib tug ua tsis taus;
• Yog hais tias ib tug neeg mob nrog cov syndrome muaj ntau thiab mob ntshav qab zib, ces nws pib ib tug metabolic teeb meem, uas ua rau yus tsis tsuas mus rau ib tug txo nyob rau hauv efficiency, tab sis kuj txo lub neej expectancy.

kev kho mob

Puas yuav ua tau los mus tshem tawm cov syndrome ntawm Morgagni-Stewart-Morel? Kev kho mob ntawm tus kab mob yog feem ntau nyob rau hauv ib tug noj cov zaub mov zoo xws li cov assignable mob ntshav qab zib thiab rog. Cov zaub mov yuav tsum tau ib tug tsawg-calorie, high-protein, vitamin thiab pob zeb hauv av ntsev. Cov khoom noj txo tus nqi ntawm cov carbohydrates thiab nqaijrog. Noj cov zaub mov Baranov yog muab mas.

Nyob rau hauv tas li ntawd, cov kev kho mob yog nqa tawm zaws thiab muab tso rau lub cev txoj kev kawm ce yuav txo cov leeg tsis muaj zog thiab ua kom peripheral ncig. Yog hais tias tus neeg mob muaj lub plawv tsis ua hauj lwm, cov kev kho mob ntawm cov syndrome tuav diuretics kardiopreparatami thiab t. D.