Marble pob txha kab mob: ua, cov tsos mob, kev kho mob, kev tiv thaiv

Marble yog ib tug congenital kab mob pathology uas yog manifested los ntawm diffuse osteosclerosis feem ntau ntawm skeletal cov pob txha thiab sib sib zog nqus hloov nyob rau hauv poov hlau-phosphorus metabolism. Tus kab mob yog tsis tshua muaj tsis tshua muaj. Nws twb xub piav nyob rau hauv 1904 los ntawm tus German kws phais neeg thiab radiologist Albers-Schoenberg (Albers-Schonberg NE). Marble kab mob no tshwm sim kiag li nyob rau hauv tag nrho cov muaj hnub nyoog pawg, nyob rau hauv lub teb chaws thoob plaws lub ntiaj teb no, ib yam li nyob rau hauv ob qho tib si kuj.

Tus kab mob muaj ib tug xov tooj ntawm txawv - congenital osteosclerosis, osteopetrosis, thiab dysplasia giperostaticheskaya Albers-Schonberg kab mob. Tsis txhob xav yuam kev rau lub marble kab mob thiab ib tug syndrome hu ua "marble daim tawv nqaij." Thaum marble pob txha kab mob nyob rau hauv lub cev pob txha pib tsim ntxiv compact yeeb tshuaj, raws li zoo raws li nyob rau hauv lub medullary kwj dej pib los tsim ib tug tuab pob txha. Ib tug marble hu ua congenital daim tawv nqaij vazonevroz hlab ntsha nyob rau hauv daim tawv nqaij, feem ntau tshwm sim nyob rau hauv cov me nyuam thiab manifests nws tus kheej reticular me ntsis rau ntawm daim tawv nqaij ib xiavlus xim tom qab quenching. Tom qab sov lub tsos mob disappears. Nws kuj tshwm sim rau cov neeg laus marble daim tawv nqaij nrog ib tug nyias lub teeb tawv nqaij uas muaj teeb meem nrog cov hlab ntsha.

Lub etiology ntawm tus kab mob no yog tsis paub hais tias. Nyob rau hauv feem ntau paub mob ntawm tus kab mob nws muaj ib tug marble tsev neeg ua cim thiab yog kis tau los ntawm tiam mus rau tiam. Nws lub npe marble kab mob tshuav ib tug tshwj xeeb daim duab ntawm X-rays ntawm lub cev pob txha, uas yog denoted los ntawm ib tug txawv txawv homogeneity thiab ntse pob txha ceev, raws li zoo raws li cov tsis muaj pob txha qauv. Nws nkawd hais tias cov pob txha no yog ua los ntawm marble.

Muaj ob hom ntawm tus kab mob marble:

- ntws nrog tsis pom kev soj ntsuam mob, thiaj paub hais tias tsuas yog X-ray xeem;

- manifests nws tus kheej nyob rau hauv thaum ntxov thaum yau, muaj cov lus hais cov tsos mob.

Lub ntsiab feature ntawm tus kab mob yog tus nruam los yog ib nrab hardening ntawm lub trabecular pob txha. Thaum thawj zaug rau theem ntawm tus kab mob xwb sclerotized tubular cov pob txha nyob rau hauv cov pob txha metaphyses thiab tiaj tus nyob rau hauv lub peripheral feem. Tsis tas li ntawd, kuaj tsis zoo tib foob cranial pob txha, lom zem ntau cov paranasal kab noj hniav, tshwj xeeb tshaj yog thawj thiab frontal. Swb yog tseem raug thiab cov txhab puab tsaig, nws yog nrog los ntawm kev ua txhaum cai ntawm qhov uas thiab hniav kev loj hlob - hloov lawv cov qauv, insufficiently tsim cov hauv paus hniav, obliterating raws thiab muaj kab noj hniav ntawm tus hniav. Feem ntau cov feem ntau cov neeg mob nrhiav kev kho mob ua mob nyob rau hauv lub ceg ntoo thiab qaug zog thaum taug kev. Marble pob txha kab mob kuj adversely muaj feem xyuam rau txoj kev loj hlob ntawm lub vascular system, raws li ntev li txoj kev loj hlob ntawm kev txawv txav pob txha cov ntaub so ntswg maj mam hloov cov hematopoietic cov ntaub so ntswg.

Qhov zoo tshaj plaws kev tshwm sim tus kab mob los kho tus mob marble twb tau nyob rau hauv cov me nyuam hloov (hloov) hlwb pob txha. Muaj tseeb tiag, zoo kev kho mob ntawm tus kab mob no tsis tam sim no ua ib ke. Kev kho mob ntawm tus kab mob no yog tsuas yog tsom ntawm strengthening lub npag thiab tshee systems, thiab nqa nyob rau hauv feem ntau raws li outpatients. Cov neeg mob qhia physiotherapy, massage thiab ua luam dej. Khoom noj khoom haus yuav tsum muaj ib daim ntawv qhia txog, nplua nuj nyob rau hauv ib txoj lw ntsiab thiab vitamins, yuav tsum muaj tam sim no nyob rau hauv cov zaub mov, cheese, txiv hmab txiv ntoo thiab zaub, tej yam ntuj tso txiv hmab txiv ntoo thiab zaub juices. Cov me nyuam nrog rau qhov no mob tsis tseg xa mus rau sanatorium kev kho mob.

Cov yooj yim txoj kev rau kev tiv thaiv tus kab mob marble koom tuav perinatal diagnostic hnub 8 lub lis piam. Yuav kom tiv thaiv qhov tshwm sim ntawm cov pob txha deformities thiab pathological cov pob txha lov yuav tsum tau nqa tawm dynamic xeem nyob rau hauv orthopedics.